Sickle Cell
What is Sickle Cell?
Sickle cell is a disorder of the haemoglobin in the red
blood cells. Haemoglobin is the substance in red blood cells that
is responsible for the colour of the cell and for carrying oxygen
around the body. People with sickle cell disorder are born with the
condition, it is not contagious. It can only be inherited from both
parents each having passed on the gene for sickle cell.
The main symptoms of sickle cell disorder are anaemia and episodes of severe pain. The pain occurs when the cells change shape after oxygen has been released. The red blood cells then stick together, causing blockages in the small blood vessels. These painful episodes are referred to as sickle cell crisis. They are treated with strong painkillers such as morphine to control the pain.
Long Term Effects
There can be a number of long term effects from sickle cell
and your team will talk to you about these and how to reduce the
risk of these complications. Treatment of sickle cell mostly
focuses on preventing and treating complications. You can
read more about complications of sickle cell here, you should talk to your team about any
worries or concerns.
The only possible cure for the disorder is a bone marrow transplant but this is only possible for a limited number of affected individuals who have a suitable donor. A medicine called Hydroxyurea, can significantly reduce the number of painful crises. Alongside your team the Sickle Cell Society can provide more information and support